Mast Cell Sarcoma

Classification	ICD-10: C96.2; ICD-10-CM: C96.22; ICD-9-CM: 202.6; ICD-O: M9740/3; MeSH: D012515; SNOMED CT: 13583002;
External resources	Orphanet: 66661;

Mast cell sarcoma
Mast cell sarcoma
Specialty	Oncology
Usual onset	Can occur at any age.
Prognosis	The median survival time is less than 18 months

Mast cell sarcoma is an extremely aggressive^[2] form of sarcoma made up of neoplastic mast cells. A sarcoma is a tumor made of cells from connective tissue. Mast cell sarcoma is an extremely rare tumor. Only three cases have been are reported so far^[when?]. Prognosis is extremely poor. People with a mast cell sarcoma have no skin lesions, and pathology examination of the tumor shows it to be very malignant with an aggressive growth pattern.^[3] Mast cell sarcoma should not be confused with extracutaneous mastocytoma, a rare benign mast cell tumor without destructive growth. In the cases observed, mast cell sarcoma terminated quickly as mast cell leukemia; one of the most aggressive human cancers.^[4]

Mast cell sarcoma, burgeoning polylobar tissue lesion of the right colon

References[edit | edit source]

↑ Monnier J., Georgin-Lavialle S., Canioni D., Lhermitte L., Soussan M., Arock M., Bruneau J., Dubreuil P., Bodemer C., Chandesris M., Lortholary O., Hermine O., Damaj G. et al Mast cell sarcoma: new cases and literature review. Oncotarget. 2016; 7: 66299-66309. Retrieved from https://www.oncotarget.com/article/11812/text/ Archived 2020-08-06 at the Wayback Machine
↑ Chott A, Guenther P, Huebner A, Selzer E, Parwaresch R, Horny H, Valent P (2003). "Morphologic and immunophenotypic properties of neoplastic cells in a case of mast cell sarcoma". Am J Surg Pathol. 27 (7): 1013–9. doi:10.1097/00000478-200307000-00019. PMID 12826896.
↑ Nancy Gould, "Diagnosis and Classification of Mastocytosis Archived 2004-10-27 at the Wayback Machine", The Mastocytosis Society.
↑ Ansell SM, ed. (2008). Rare Hematological Malignancies. Cancer Treatment & Research. Springer.

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[1] Monnier J., Georgin-Lavialle S., Canioni D., Lhermitte L., Soussan M., Arock M., Bruneau J., Dubreuil P., Bodemer C., Chandesris M., Lortholary O., Hermine O., Damaj G. et al Mast cell sarcoma: new cases and literature review. Oncotarget. 2016; 7: 66299-66309. Retrieved from https://www.oncotarget.com/article/11812/text/ Archived 2020-08-06 at the Wayback Machine

[2] Chott A, Guenther P, Huebner A, Selzer E, Parwaresch R, Horny H, Valent P (2003). "Morphologic and immunophenotypic properties of neoplastic cells in a case of mast cell sarcoma". Am J Surg Pathol. 27 (7): 1013–9. doi:10.1097/00000478-200307000-00019. PMID 12826896.

[3] Nancy Gould, "Diagnosis and Classification of Mastocytosis Archived 2004-10-27 at the Wayback Machine", The Mastocytosis Society.

[4] Ansell SM, ed. (2008). Rare Hematological Malignancies. Cancer Treatment & Research. Springer.

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Classification	ICD-10: C96.2 ICD-10-CM: C96.22 ICD-9-CM: 202.6 ICD-O: M9740/3 MeSH: D012515 SNOMED CT: 13583002
External resources	Orphanet: 66661

Mast Cell Sarcoma

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